"Turricephaly"

Single-stage Total Cranial Vault Remodeling for Correction of Turricephaly: Description of a New Technique Turricephaly is considered one of the most difficult cranial deformities to correct as addressing cranial height can result in increased intracranial pressure. We describe a new technique of total calvarial remodeling with bony transposition to simultaneously correct turricephaly cranial height reduction achieved was 1.6 cm (range, 1.0-2.0 cm), and mean anterior-posterior expansion was 3.4 cm (range, 2.3-4.5 cm). Patients also showed improvement in supraorbital retrusion. Single-stage cranial vault remodeling with axial strip craniectomy and coronal interposition is safe and allows for simultaneous correction of turricephaly and brachycephaly while preserving intracranial volume.

; this is usually preparation for maxillary surgery.Apert SyndromeIn nearly all patients with Apert syndrome, the cause is 1 of 2 FGFR2 mutations involving amino acids (Ser252Trp, Pro253Arg). The condition is inherited in an autosomal dominant mode. [8] Craniosynostosis is present, characterized by brachycephaly and, frequently, turricephaly; the anterior fontanelle is enlarged. [9] The maxilla is hypoplastic are considered separately.Common deformities that occur as a result of premature suture fusion are scaphocephaly, trigonocephaly, brachycephaly, plagiocephaly, oxycephaly, and turricephaly. The sutures involved in these deformities are sagittal, metopic, bicoronal, unicoronal, and multiple for the last 2 conditions. Complex premature suture fusion is associated with Apert, Crouzon, Kleeblattschädel, Pfeiffer

manifestations occur. (B) Premature fusion of all the cranial sutures causes turricephaly. The skull has nowhere to grow but up. View Media Gallery * * Lambdoid suture - Occipital plagiocephaly * * Multiple cranial sutures - Acrocephaly, turricephaly (see image above), oxycephaly * * Kleeblattschädel anomaly (all with different phenotypic appearances) Syndromic dysostoses are associated

the recession of the frontoorbital bar and turricephaly. View Media Gallery Craniosynostosis management. Frontal view of a 3-dimensional CT scan demonstrating turricephaly and recession of the frontoorbital bar. View Media Gallery Craniosynostosis management. Superior view of a 3-dimensional CT scan demonstrating bicoronal synostosis with significant recession of the frontoorbital bar and the frontal bones craniosynostosis demonstrating frontal bossing bilaterally and dolichocephaly. View Media Gallery Brachycephaly or "short skull" occurs secondary to fusion of both coronal sutures (see the images below). Fusion of both coronal sutures prevents anteroposterior growth of the calvarium and the anterior cranial fossa. The calvarium tends to grow vertically, leading to turricephaly, and laterally, leading

anterior turricephaly and corrects frontal bossing and brachycephaly in patients with bilateral coronal craniosynostosis. Therapeutic, IV.

; this is usually preparation for maxillary surgery.Apert SyndromeIn nearly all patients with Apert syndrome, the cause is 1 of 2 FGFR2 mutations involving amino acids (Ser252Trp, Pro253Arg). The condition is inherited in an autosomal dominant mode. [8] Craniosynostosis is present, characterized by brachycephaly and, frequently, turricephaly; the anterior fontanelle is enlarged. [9] The maxilla is hypoplastic are considered separately.Common deformities that occur as a result of premature suture fusion are scaphocephaly, trigonocephaly, brachycephaly, plagiocephaly, oxycephaly, and turricephaly. The sutures involved in these deformities are sagittal, metopic, bicoronal, unicoronal, and multiple for the last 2 conditions. Complex premature suture fusion is associated with Apert, Crouzon, Kleeblattschädel, Pfeiffer

manifestations occur. (B) Premature fusion of all the cranial sutures causes turricephaly. The skull has nowhere to grow but up. View Media Gallery * * Lambdoid suture - Occipital plagiocephaly * * Multiple cranial sutures - Acrocephaly, turricephaly (see image above), oxycephaly * * Kleeblattschädel anomaly (all with different phenotypic appearances) Syndromic dysostoses are associated

the recession of the frontoorbital bar and turricephaly. View Media Gallery Craniosynostosis management. Frontal view of a 3-dimensional CT scan demonstrating turricephaly and recession of the frontoorbital bar. View Media Gallery Craniosynostosis management. Superior view of a 3-dimensional CT scan demonstrating bicoronal synostosis with significant recession of the frontoorbital bar and the frontal bones craniosynostosis demonstrating frontal bossing bilaterally and dolichocephaly. View Media Gallery Brachycephaly or "short skull" occurs secondary to fusion of both coronal sutures (see the images below). Fusion of both coronal sutures prevents anteroposterior growth of the calvarium and the anterior cranial fossa. The calvarium tends to grow vertically, leading to turricephaly, and laterally, leading

of a closure of both the coronal sutures.[11] Following Virchow's law, this will result in a child's head with a restriction of growth in the forward direction and in the backward direction: recessed frontal bones and a flattened occiput.[11] Compensatory growth will occur sideways, due to the sagittal suture, and upwards, due to the lambdoid sutures.[11]Oxycephaly[edit]Oxycephaly, also known as turricephaly