Postnatal Outcomes in Prenatally Detected VascularRings. Vascularrings are rare congenital defects that can cause tracheal and/or esophageal compression. Prenatal detection is increasing due to advances in screening and fetal echocardiography. Postnatal outcomes remain variable. We describe our single-center experience of postnatal outcomes in prenatally detected vascularrings and evaluate factors associated with surgery. We performed a retrospective review of all fetal diagnoses of possible vascularring evaluated between 2016 and 2023. Patients with significant intracardiac abnormalities, without postnatal data, or without confirmed postnatal diagnosis were excluded from postnatal analysis. Outcome variables included symptoms, tracheal/esophageal compression, and surgical repair
Long-term Outcomes Following Thoracoscopic Division of VascularRings. We evaluate long-term symptomatic improvement in vascularring patients who underwent thoracoscopic division at a single quaternary pediatric surgery center. All pediatric patients who underwent vascularring division without Kommerell's diverticulum resection between 01/2007-12/2022 were included. Surgeries were performed with an aberrant LSCA without Kommerell's resection may be adequate to ensure long-term improvement of breathing and swallowing problems attributable to vascularrings. Level IV.
Variations in the Evaluation and Management of VascularRings: A Survey of American Clinicians. Vascularrings are arterial malformations that lead to the compression of the trachea and/or esophagus. While "tight" rings often produce symptoms and require surgery, "loose" rings rarely produce symptoms. Given advances in fetal echocardiography, this diagnosis is now more often made prenatally cardiothoracic surgeons. Survey questions targeted respondent practice characteristics, testing obtained, and indications for testing or surgical referral. In total 61 responses were received, predominantly from pediatric cardiologists (95%) in the United States (97%). About 60% of clinicians reported frequently diagnosing patients with vascularrings by fetal echocardiogram, with only about 20% diagnosing
Outcomes of Patients Undergoing Surgery for Complete VascularRings. Few studies describe outcomes after complete vascularring surgery in a comprehensive manner. This study sought to describe the clinical presentation, diagnostic work-up, operative approach, and outcomes in children undergoing surgery for complete vascularrings. This single-center retrospective cohort study includes consecutive patients (January 1990 through September 2023) undergoing primary surgery for complete vascularrings, or rerepair after primary surgery elsewhere. The primary outcome of interest was complete (as distinct from partial) symptom resolution at latest clinic follow-up. Our current preference is to pursue a comprehensive initial operation including adjunctive vascular and airway procedures targeting
Vascularring: prenatal diagnosis and prognostic management based on sequential cross-sectional scanning by ultrasound. In terms of embryonic origin, vascularring is a congenital anomaly in which the aortic arch and its branches completely or incompletely encircle and compress the trachea or esophagus. Early and accurate diagnosis of a vascularring is the key to treatment. Prenatal diagnosis axis of the body until the superior mediastinum had disappeared. If a vascularring was found, the shape of the ring and the distance of the branch to the airway were observed. The distance relationship with the airway was divided into three grades: I-III; the closer the distance, the lower the grade. The vascularrings were monitored every 4 weeks before birth. All were monitored before surgery or 1
Contemporary Outcomes in Fetuses Diagnosed with VascularRings. Vascularrings are increasingly identified on fetal echocardiography. The purpose of this study is to analyze clinical outcomes and patterns of diagnostic testing in fetuses with vascularrings diagnosed by echocardiography. A retrospective cohort study was performed of fetuses with postnatally confirmed vascularrings from 2017 arch). A vascularring was isolated in 59%, associated with structural heart lesions in 33%, and associated with noncardiac anomalies in 8%. Prenatal diagnoses increased over time. Symptoms developed in 24% (11/46); 82% (9/11) had respiratory and 45% (5/11) had gastroesophageal complaints. Surgery was performed in 17% (11/46). Symptoms presented bimodally, prior to 100 or after 400 days of life
Persistence of aerodigestive symptoms after vascularring repair. Vascularrings are often associated with respiratory and swallowing difficulties due to tracheal or esophageal compression. While the results of a vascularring repair are considered excellent, the long-term effect of tracheal and esophageal remodeling and the persistence of symptoms have scarcely been reported. Our study aims to evaluate the respiratory and swallowing outcomes of vascularring repair. A retrospective cohort study of children who underwent vascularring repair between 2010 and 2022 in a tertiary-care children's hospital. There were 108 patients enrolled: sixty-three patients (57.41 %) with a right aortic arch, 42 patients (38.89 %) with a double aortic arch, and 3 patients (2.78 %) with other vascularrings
Unusual VascularRing in the Fetus. We present the clinical course and echocardiographic and genetic findings of two fetuses with an unusual vascularring, created by a left aortic arch with a right arterial duct and an aberrant right subclavian artery. One fetus was diagnosed with 22q11.2 microdeletion and the other became symptomatic in infancy. It is important to consider the position of the arterial ductal ligament in patients who present with tracheoesophageal compressive symptoms in the presence of a left aortic arch. These cases also highlight that a vascularring formed from a left arch may have similar associations to a vascularring formed by a right aortic arch.
Narrowing Down the Symptomatology of Isolated VascularRings in Children. Vascularrings may cause respiratory or gastrointestinal symptoms due to compression of the trachea and/or esophagus. Advances in imaging have enabled early detection in asymptomatic patients posing new management dilemmas. Surgery is expected to relieve symptoms, although this has not been well studied. We sought to evaluate the presence and pattern of symptoms associated with vascularrings before surgical intervention and to detail symptom resolution after surgery. A 10-year retrospective review of patients diagnosed with an isolated vascularring was performed between January 2010 and December 2019. 100 patients were identified; 35 double aortic arch (DAA) and 65 right aortic arch and left ligamentum arteriosum
3D printing of foetal vascularrings: feasibility and applicability. Vascularrings (VRs) exhibit complex and diverse forms that are difficult to conceptualize using traditional two-dimensional (2D) schematic. Inexperienced medical students and parents who lack a medical technology background face significant challenges in understanding VRs. The purpose of this research is to develop three
Influence of Fetal Diagnosis on Management of VascularRings. Fetal diagnoses of vascularrings have been increasing. We compared management strategies and outcomes of infants with fetal diagnosis with those with postnatal diagnosis to inform recommendations regarding optimal management. A retrospective review was performed of vascularring operations from January 2000 to June 2019. Standard diagnosis were significantly younger at the time of surgery (13.1 months [interquartile range (IQR), 20.6] vs 24.0 months [IQR, 87.0], P = .029). There was no difference in postoperative complications or length of stay (3 days [IQR, 1] for fetal diagnoses vs 4 days [IQR, 3] for postnatal diagnoses, P = .50). Fetal diagnosis leads to the potential for expectant management of vascularring patients
Reoperation to correct unsuccessful vascularring and vascular decompression surgery. Although most children do well after operations to relieve vascular compression of the esophagus and airway, many will have persistent/recurrent symptoms. We review our surgical experience using a customized approach to correct various etiologies of failure after vascularring/decompression surgery. Our institutional database identified children who underwent reoperation for persistent/recurrent symptoms after vascularring or aberrant arterial decompression surgery between January 2014 and December 2019. Charts were reviewed for operative approaches and clinical data. Findings were analyzed by Fisher exact test for comparison between groups. Twenty-seven children required reoperative surgery. Detailed
Symptom persistence after vascularring repair in children. Vascularrings are often diagnosed after evaluation for swallowing and breathing difficulties. Data regarding symptoms following vascularring repair is sparse. We sought to determine whether symptoms persist using chart review and a survey. Sixty-three patients underwent open vascularring repair from July 2007 to May 2018. Data DAA). Five SAA had breathing and swallowing symptoms, and 3 SAA and 3 DAA had breathing difficulties. Open vascularring repair remains a safe repair. However, further investigation of the persistent symptoms in these patients is merited. Retrospective Comparative Study, Level III.
Right Aortic Arch in VascularRing Defects Right Aortic Arch in VascularRing Defects: Background, Epidemiology, Etiology For YouNews & PerspectiveDrugs & DiseasesCME & EducationAcademyVideoDecision PointEdition:EnglishMedscapeEnglishDeutschEspañolFrançaisPortuguêsUKNewUnivadisLog In Sign Up It's Free!English EditionMedscape * English * Deutsch * Español * Français * Português =aHR0cHM6Ly9lbWVkaWNpbmUubWVkc2NhcGUuY29tL2FydGljbGUvODk5NzQ1LW92ZXJ2aWV3processing....Drugs & Diseases > Pediatrics: Cardiac Disease and Critical Care Medicine Right Aortic Arch in VascularRing DefectsUpdated: Jan 10, 2020 * Author: Doff B McElhinney, MD; Chief Editor: Howard S Weber, MD, FSCAI more... * * Share * Email * Print * FeedbackClose * Facebook * Twitter * LinkedIn * WhatsAppSections Right Aortic Arch in VascularRing Defects * * Sections Right Aortic Arch
VascularRing and Sling Surgery VascularRing and Sling Surgery: Historical Perspective, Embryology, Abnormalities For YouNews & PerspectiveDrugs & DiseasesCME & EducationAcademyVideoDecision PointEdition:EnglishMedscapeEnglishDeutschEspañolFrançaisPortuguêsUKNewUnivadisLog In Sign Up It's Free!English EditionMedscape * English * Deutsch * Español * Français * Português * UKNewUnivadisXUnivadis =aHR0cHM6Ly9lbWVkaWNpbmUubWVkc2NhcGUuY29tL2FydGljbGUvOTA0MzEzLW92ZXJ2aWV3processing....Drugs & Diseases > Pediatrics: Cardiac Disease and Critical Care Medicine VascularRing and Sling SurgeryUpdated: Jun 13, 2017 * Author: Mary C Mancini, MD, PhD, MMM; Chief Editor: Suvro S Sett, MD, FRCSC, FACS more... * * Share * Email * Print * FeedbackClose * Facebook * Twitter * LinkedIn * WhatsAppSections VascularRing and Sling Surgery * * Sections VascularRing and Sling Surgery
VascularRings in Adults: Outcome of Surgical Management. Limited data exist on the management of vascularrings (VR) in adults. We reviewed our experience of surgical treatment of these patients. All adult patients with VR (n = 65) who underwent VR repair (mean age, 45 ± 16 years; 33 women [51%]) from January 1972 to January 2018 were retrospectively reviewed. Anatomic variants were right arch
Contemporary Mid-term Outcomes in Pediatric Patients undergoing VascularRing Repair. This single-institution study assessed the midterm outcomes of patients undergoing complete vascularring (CVR) repair and the need for reintervention. The study included all patients who underwent surgical repair of an isolated CVR from 1996 to 2018 at our institution. Patients who underwent concomitant
Prenatal Detection, Comorbidities, and Management of VascularRings. The 3-vessel and trachea view is now integrated into obstetrical screening and facilitates prenatal detection of vascularrings. We examined trends in prenatal detection, associated cardiac and extracardiac anomalies, and surgical management in this population. We reviewed a population-based cohort of pediatric vascularring (24/28vs 53/78, p = 0.04) and associated cardiac pathology (18/28vs 33/78, p = 0.05). The rate of genetic anomalies was overall higher than previously reported (34%) and did not differ between groups (11/28vs 25/78, p = 0.48). Those with a prenatal diagnosis were less likely to require cross-sectional imaging (9/28vs 48/78, p <0.01), modifying the vascularring subtype diagnosis in 2 patients
Vascularring: Early and long-term mortality and morbidity after surgical repair. Vascularring is a rare cause of recurrent respiratory infections, dysphagia and stridor. Surgical repair is considered safe but the long-term outcomes are unclear. The purpose of this study was to investigate the mortality and morbidity following vascularring surgery in a single institution. This retrospective study covers operations done at Aarhus University Hospital, Denmark between October 1983 and May 2015. Medical records were reviewed focusing on early complications and long-term complaints up to September 2017. A total of 23 patients with median age of 1.4 years (range 0.008-64 years) were operated for vascularring. Median follow-up was 6.8 years (range 2.4-34 years). Presenting symptoms were